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      • 目錄號(hào) : TW1332
      • 應(yīng)用 : 僅限于科研使用
      • 貨期 : 現(xiàn)貨
      • 規(guī)格 ：100ul/200ul/25ul
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    中文名稱： 兔抗GCH1多克隆抗體
       

    英文名稱： Anti-GCH1 rabbit polyclonal antibody


    別      名： GCH, DYT5, DYT14, DYT5a, GTPCH1, HPABH4B, GTP-CH-1


    相關(guān)類別： 一抗


    儲(chǔ)      存： 冷凍（-20℃）
    宿       主： Rabbit


    抗       原： GCH1

    反應(yīng)種屬： Human


    標(biāo)  記  物： Unconjugate


    克隆類型： rabbit polyclonal


    技術(shù)規(guī)格

    Background:

    This gene encodes a member of the GTP cyclohydrolase family. The encoded protein is the first and rate-limiting enzyme in tetrahydrobiopterin (BH4) biosynthesis, catalyzing the conversion of GTP into 7,8-dihydroneopterin triphosphate. BH4 is an essential cofactor required by aromatic amino acid hydroxylases as well as nitric oxide synthases. Mutations in this gene are associated with malignant hyperphenylalaninemia and dopa-responsive dystonia. Several alternatively spliced transcript variants encoding different isoforms have been described; however, not all variants give rise to a functional enzyme.

    Applications:

    ELISA, WB, IHC

    Name of antibody:

    GCH1

    Immunogen:

    Synthetic peptide of human GCH1

    Full name:

    GTP cyclohydrolase 1

    Synonyms：

    GCH, DYT5, DYT14, DYT5a, GTPCH1, HPABH4B, GTP-CH-1

    SwissProt:

    P30793

    ELISA Recommended dilution:

    1000-5000

    IHC positive control:

    Human breast cancer

    IHC Recommend dilution:

    5-20

    WB Predicted band size:

    28 kDa

    WB Positive control:

    Human fetal liver tissue

    WB Recommended dilution:

    500-2000